African Journal of Paediatric Surgery About APSON | PAPSA  
Home About us Editorial Board Current issue Search Archives Ahead Of Print Subscribe Instructions Submission Contact Login 
Users Online: 1248Print this page  Email this page Bookmark this page Small font size Default font size Increase font size 
 
CASE REPORT
Year : 2014  |  Volume : 11  |  Issue : 4  |  Page : 341-346

Spinal and pelvic corrections in a patient with spondylocostal dysplasia syndrome and hemimyelomeningocele


1 Department of First Medical, Ludwig Boltzmann Institute of Osteology, at the Hanusch Hospital of WGKK and, AUVA Trauma Centre Meidling, Hanusch Hospital; Department of Paediatric, Orthopaedic Hospital of Speising, Vienna, Austria
2 Department of Orthopaedics, Hamburg-Eppendorf and Pediatric Orthopaedic Department, Childrens Hospital, Hamburg-Altona, University Medical Center, Hamburg, Germany
3 Department of Paediatric, Orthopaedic Hospital of Speising, Vienna, Austria
4 Department of First Medical, Ludwig Boltzmann Institute of Osteology, at the Hanusch Hospital of WGKK and, AUVA Trauma Centre Meidling, Hanusch Hospital, Vienna, Austria

Correspondence Address:
Dr. Ali Al Kaissi
Department of Paediatric, Orthopaedic Hospital of Speising, Vienna
Austria
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0189-6725.143163

Rights and Permissions

Congenital malformation complex of the spine and the spinal cord can be a syndromic entity rather than a symptom complex. The spinal cord lesion is usually bilaterally symmetrical, but, there are occasional cases with one or more hemivertebrae, often associated with a central bony spur splitting the cord (diastematomyelia), in which one leg is virtually normal while the other is severely paralysed. Hemimyelomeningocele over the lumbar area may be associated with extensive spine malsegmentation compatible with the diagnosis of spondylocostal dysplasia syndrome. In this report, we present a 3-year-old girl who underwent neurological evaluation and spinal imaging studies for extensive spine malsegmentation compatible with spondylocostal dysostosis syndrome associated with hemimyelomeningocele. She had a series of corrective orthopaedic interventions to reconstruct her pelvic girdle and spine deformities, with a satisfactory outcome.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed2659    
    Printed47    
    Emailed0    
    PDF Downloaded108    
    Comments [Add]    

Recommend this journal